Diab Kh.M., Daikhes N.A., Saydulaev V.S., Yunusov A.S., Pashinina O.A., Umarov P.U., Panina O.S. Juvenile paraganglioma. Head and neck. Russian Journal. 2022;10(3):76–80
Juvenile paraganglioma is an extremely rare condition of the temporal bone. Due to the lack of specific symptoms, timely diagnosis is delayed, and the disease is detected at late stages. Inflammatory diseases of the middle and external ear commonly mask the clinic of paraganglioma in children. Juvenile paraganglioma is characterized by aggressive growth. Treatment depends on many factors; in most cases, surgical treatment is used.
Clinical case description. The two-year-old patient was admitted for treatment to the Ear and Skull Base Disease Department of the Federal State Budgetary Institution of the National Medical Research Center of Otorhinolaryngology of the FMBA of the Russian Federation in January 2019 with complaints on hearing loss, pulsatile tinnitus, discomfort in the left ear. Diagnosis: Juvenile paraganglioma. Surgical treatment was performed: removal of the tumor using a combined micro-endoscopic transotic approach. The erosion of bony walls of internal carotid artery and internal jugular vein was observed. Using angiolytic laser helped the surgeon to minimize intraoperative bleeding. Pathological examination of the removed tissue confirmed the diagnosis of juvenile paraganglioma.
Сonclusion. Paraganglioma is an extremely rare tumor in pediatric patients. Many authors consider juvenile paraganglioma in children to be a congenital condition. Paraganglioma in children is characterized by an extremely high frequency of diagnostic errors, as evidenced by the clinical cases described in the literature. Every otorhinolaryngologist should be aware of this rare condition.
Key words: juvenile paraganglioma, middle ear, angiolytic laser, tympanic cavity
Conflict of interest. The authors declare that there is no conflict of interest.
Funding. There was no funding for this study.