Vlasova G.V., Pavlov P.V. Congenital cholesteatoma of the middle ear in children: clinical manifestations. Head and neck. Russian Journal. 2023;11(3):23–27
The article provides a retrospective analysis of complaints, case history, and examination results of 33 children from 1 to 10 years old who received surgical treatment for congenital cholesteatoma (СC) of the middle ear. The purpose was to identify the features of its clinical manifestation. The congenital nature of cholesteatoma was established using the Levenson criteria. CC was found in 19% of the total cholesteatomas operated in the Clinic. The presence of middle ear inflammation or suppuration in case history or at the time of admission was noted in 82% of patients. In 6 patients (16%), the first symptoms of CC were facial nerve paresis, sepsis, periostitis of the mastoid process. Conclusion. The manifestation of CC as an acute middle ear inflammation is quite typical in children. Secondary infection of CC against the background of acute inflammation of the middle ear is the reason for the conservative treatment inefficacy and leads to perforation of the tympanic membrane and other complications. CC is characterized by pronounced bone destruction in the middle ear developing over a short time period.
Key words: congenital cholesteatoma, inflammation of the middle ear
Conflicts of interest. The authors have no conflicts of interest to declare.
Funding. There was no funding for this study